[Lattice corneal dystrophy. Detection of a point mutation in the kerato-epithelin gene]

Ophthalmologe. 1999 Jun;96(6):405-7. doi: 10.1007/s003470050426.
[Article in German]

Abstract

Background: Lattice dystrophy is an autosomal-dominantly inherited disease. A mutation of the gene coding for kerato-epithelin has been found in patients with this stromal dystrophy. In codon 124 a Guanine to Adenine mutation of the nucleotide 417 has been described. We looked for this mutation in a family with lattice dystrophy treated in our clinic.

Patients and methods: Using primers specific for kerato-epithelin gene, we amplified the cDNA extracted from lymphocytes of two patients suffering from lattice dystrophy. The polymerase chain reaction (PCR) products were subcloned and sequenced.

Results: Guanine to Adenine mutations, as published were detected in both of our patients at codon 124.

Conclusion: We found the published mutation in both of our patients, indicating that this Guanine to Adenine exchange is pathognomonic for lattice dystrophy.

Publication types

  • English Abstract

MeSH terms

  • Chromosome Aberrations / genetics
  • Chromosome Disorders
  • Codon / genetics
  • Corneal Dystrophies, Hereditary / genetics*
  • Female
  • Genes, Dominant / genetics
  • Humans
  • Keratins / genetics*
  • Point Mutation / genetics*
  • Polymerase Chain Reaction

Substances

  • Codon
  • Keratins