Kinetics of prion protein accumulation in the CNS of mice with experimental scrapie

J Neuropathol Exp Neurol. 1999 Dec;58(12):1244-9. doi: 10.1097/00005072-199912000-00005.

Abstract

The kinetics of PrP(Sc) and insoluble PrP accumulation in the spleens and brains of CD-1 mice were studied. The mice were inoculated intracerebrally with RML prions and euthanized at various times between inoculation and the onset of illness at approximately 130 days. Protease-resistant PrP(Sc), PrP 27-30, was first detected in brain by histoblotting 49 days after inoculation and by Western immunoblotting at 70 days. In spleen, PrP 27-30 was first detected by Western immunoblotting at 28 days after inoculation. Like PrP 27-30, substantial increases in detergent-insoluble PrP were first detected at 70 days after inoculation in brain and 28 days in spleen. In addition, a progressive increase in detergent-soluble PrP was detected beginning 70 days after inoculation. Further characterization of detergent soluble and insoluble PrP with respect to protease-sensitive PrP(Sc) and prion infectivity will be of considerable interest.

MeSH terms

  • Animals
  • Blotting, Western
  • Brain / metabolism*
  • Detergents / pharmacology
  • Kinetics
  • Mice
  • PrP 27-30 Protein / metabolism
  • PrPSc Proteins / metabolism
  • Prions / metabolism*
  • Scrapie / metabolism*
  • Solubility
  • Spleen / metabolism
  • Time Factors
  • Tissue Distribution

Substances

  • Detergents
  • PrPSc Proteins
  • Prions
  • PrP 27-30 Protein