Interleukin-9 upregulates mucus expression in the airways

Am J Respir Cell Mol Biol. 2000 Jun;22(6):649-56. doi: 10.1165/ajrcmb.22.6.3927.

Abstract

Interleukin (IL)-9 has recently been shown to play an important role in allergic disease because its expression is strongly associated with the degree of airway responsiveness and the asthmatic-like phenotype. IL-9 is a pleiotropic cytokine that is active on many cell types involved in the allergic immune response. Mucus hypersecretion is a clinical feature of chronic airway diseases; however, the mechanisms underlying the induction of mucin are poorly understood. In this report, we show that IL-9 regulates the expression of a subset of mucin genes in lung cells both in vivo and in vitro. In vivo, the constitutive expression of IL-9 in transgenic mice results in elevated MUC2 and MUC5AC gene expression in airway epithelial cells and periodic acid-Schiff-positive staining (reflecting mucous glycogenates). Similar results were observed in C57BL/6J mice after IL-9 intratracheal instillation. In contrast, instillation of the T helper 1-associated cytokine interferon gamma failed to induce mucin production. In vitro, our studies showed that IL-9 also induces expression of MUC2 and MUC5AC in human primary lung cultures and in the human muccoepidermoid NCI-H292 cell line, indicating a direct effect of IL-9 on inducing mucin expression in these cells. Altogether, these results suggest that upregulation of mucin by IL-9 might contribute to the pathogenesis of human inflammatory airway disorders, such as asthma. These data extend the role of the biologic processes that IL-9 has on regulating the many clinical features of asthma and further supports the IL-9 pathway as a key mediator of the asthmatic response.

MeSH terms

  • Animals
  • Asthma / immunology
  • Asthma / metabolism*
  • Carcinoma, Squamous Cell
  • DNA Primers
  • Epithelial Cells / immunology
  • Epithelial Cells / metabolism
  • Gene Expression / immunology
  • Glycoproteins / genetics
  • Glycoproteins / immunology
  • Glycoproteins / metabolism
  • Goblet Cells / immunology
  • Goblet Cells / metabolism
  • Humans
  • Hypersensitivity / immunology
  • Hypersensitivity / metabolism*
  • Interferon-gamma / immunology
  • Interferon-gamma / metabolism
  • Interleukin-13 / immunology
  • Interleukin-13 / metabolism
  • Interleukin-9 / genetics
  • Interleukin-9 / immunology
  • Interleukin-9 / metabolism*
  • Lung / cytology
  • Lung / immunology
  • Lung / metabolism
  • Mice
  • Mice, Inbred C57BL
  • Mice, Transgenic
  • Mucin 5AC
  • Mucin-2
  • Mucins / genetics
  • Mucins / immunology
  • Mucins / metabolism
  • Mucus / immunology
  • Mucus / metabolism*
  • Polymerase Chain Reaction
  • Respiratory Mucosa / immunology
  • Respiratory Mucosa / metabolism*
  • Tumor Cells, Cultured

Substances

  • DNA Primers
  • Glycoproteins
  • Interleukin-13
  • Interleukin-9
  • MUC2 protein, human
  • MUC5AC protein, human
  • Muc2 protein, mouse
  • Muc5ac protein, mouse
  • Mucin 5AC
  • Mucin-2
  • Mucins
  • Interferon-gamma