Energy landscape theory for Alzheimer's amyloid beta-peptide fibril elongation

Proteins. 2001 Feb 1;42(2):217-29. doi: 10.1002/1097-0134(20010201)42:2<217::aid-prot90>3.0.co;2-n.

Abstract

Recent experiments on the kinetics of deposition and fibril elongation of the Alzheimer's beta-amyloid peptide on preexisting fibrils are analyzed. A mechanism is developed based on the dock-and-lock scheme recently proposed by Maggio and coworkers to organize their experimental observations of the kinetics of deposition of beta-peptide on preexisting amyloid fibrils and deposits. Our mechanism includes channels for (1) a one-step prion-like direct deposition on fibrils of activated monomeric peptide in solution, and (2) a two-step deposition of unactivated peptide on fibrils and subsequent reorganization of the peptide-fibril complex. In this way, the mechanism and implied "energy landscape" unify a number of schemes proposed to describe the process of fibril elongation. This beta-amyloid landscape mechanism (beta ALM) is found to be in good agreement with existing experimental data. A number of experimental tests of the mechanism are proposed. The mechanism leads to a clear definition of overall equilibrium or rate constants in terms of the energetics of the elementary underlying processes. Analysis of existing experimental data suggests that fibril elongation occurs through a two-step mechanism of nonspecific peptide absorption and reorganization. The mechanism predicts a turnover in the rate of fibril elongation as a function of temperature and denaturant concentration. Proteins 2001;42:217-229.

Publication types

  • Comparative Study
  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, Non-P.H.S.

MeSH terms

  • Alzheimer Disease / metabolism*
  • Amyloid beta-Peptides / chemistry*
  • Amyloid beta-Peptides / genetics
  • Cross-Linking Reagents / chemistry
  • Diffusion
  • Humans
  • Kinetics
  • Models, Chemical
  • Molecular Conformation
  • Mutation
  • Peptides / chemistry
  • Peptides, Cyclic / chemistry
  • Protein Denaturation
  • Protein Folding
  • Solvents / chemistry
  • Temperature
  • Thermodynamics
  • Viscosity

Substances

  • Amyloid beta-Peptides
  • Cross-Linking Reagents
  • Peptides
  • Peptides, Cyclic
  • Solvents