Ross syndrome plus: beyond horner, Holmes-Adie, and harlequin

Neurology. 2000 Dec 26;55(12):1841-6. doi: 10.1212/wnl.55.12.1841.

Abstract

Background: Ross syndrome is an uncommon disorder characterized by the triad of segmental anhidrosis, hyporeflexia, and tonic pupils.

Methods: The authors describe the clinical findings of five patients with Ross syndrome and detail the results of their pharmacologic and autonomic testing.

Results: In four patients, the classic findings of Ross syndrome were accompanied by Horner's syndrome. Other symptoms of dysautonomia were also common.

Conclusions: These findings suggest that Ross syndrome is a dysautonomic condition of varying expression resulting from a generalized injury to ganglion cells or their projections.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Adult
  • Female
  • Heart Rate / physiology
  • Horner Syndrome / physiopathology*
  • Humans
  • Hypohidrosis / physiopathology*
  • Male
  • Middle Aged
  • Parasympathetic Fibers, Postganglionic / physiopathology*
  • Sweating / physiology*
  • Syndrome