The serpin inhibitory mechanism is critically dependent on the length of the reactive center loop

J Biol Chem. 2001 Jul 20;276(29):27541-7. doi: 10.1074/jbc.M102594200. Epub 2001 Apr 26.

Abstract

The recent crystallographic structure of a serpin-protease complex revealed that protease inactivation results from a disruption of the catalytic site architecture caused by the displacement of the catalytic serine. We hypothesize that inhibition depends on the length of the N-terminal portion of the reactive center loop, to which the active serine is covalently attached. To test this, alpha(1)-antitrypsin Pittsburgh variants were prepared with lengthened and shortened reactive center loops. The rates of inhibition of factor Xa and of complex dissociation were measured. The addition of one residue reduced the stability of the complex more than 200,000-fold, and the addition of two residues reduced it by more than 1,000,000-fold, whereas the deletion of one or two residues lowered the efficiency of inhibition and increased the stability of the complex (2-fold). The deletion of more than two residues completely converted the serpin into a substrate. Similar results were obtained for the alpha(1)-antitrypsin variants with thrombin and for PAI-1 and PAI-2 with their common target tissue plasminogen activator. We conclude that the length of the serpin reactive center loop is critical for its mechanism of inhibition and is precisely regulated to balance the efficiency of inhibition and stability of the final complex.

MeSH terms

  • Amino Acid Sequence
  • Catalytic Domain
  • Crystallography, X-Ray
  • Electrophoresis, Polyacrylamide Gel
  • Factor Xa Inhibitors
  • Humans
  • Kinetics
  • Mutagenesis
  • Protein Conformation
  • Sequence Homology, Amino Acid
  • Serpins / chemistry
  • Serpins / metabolism*
  • alpha 1-Antitrypsin / chemistry
  • alpha 1-Antitrypsin / genetics
  • alpha 1-Antitrypsin / metabolism

Substances

  • Factor Xa Inhibitors
  • Serpins
  • alpha 1-Antitrypsin