Antigen inhalation as a triggering factor in systemic small-sized-vessel vasculitis. Four cases

Ann Med Interne (Paris). 2001 Apr;152(3):152-6.

Abstract

In order to identify small-sized-vessel vasculitis occurring immediately after massive inhalation of particles which could be considered antigenic, we performed a retrospective review of patients who consulted our Department of Internal Medicine between 1980 and 1998 and were diagnosed as having small-vessel vasculitis that developed immediately after massive exposure to inhaled particles. Four patients, 27 to 55 years old, presented with small-sized-vessel vasculitis (one with Wegener's granulomatosis and three with Churg-Strauss syndrome) which developed after massive inhalation of particles. Clinical manifestations occurred from a few hours to 10 days after inhalation of diesel fumes, cereal dust, flour or cereal dust and/or pigeon droppings. Three patients remain disease-free 8, 9 and 18 years after discontinuing treatment. One patient remains well after 3 years on low-dose corticosteroids and cyclophosphamide therapy. Our data suggest that primary antigens can cause small-sized-vessel vasculitides. Identifying such etiological factors could improve our understanding of the pathogenesis of systemic vasculitides and prevent relapses due to similar antigenic exposure.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Animals
  • Anti-Inflammatory Agents / therapeutic use
  • Antigens / adverse effects*
  • Churg-Strauss Syndrome / diagnosis
  • Churg-Strauss Syndrome / etiology
  • Churg-Strauss Syndrome / therapy
  • Columbidae*
  • Combined Modality Therapy
  • Cyclophosphamide / therapeutic use
  • Dust / adverse effects*
  • Dyspnea / etiology
  • Edible Grain / adverse effects*
  • Feces*
  • Female
  • Fever / etiology
  • Flour*
  • Granulomatosis with Polyangiitis / diagnosis
  • Granulomatosis with Polyangiitis / etiology
  • Granulomatosis with Polyangiitis / therapy
  • Humans
  • Immunosuppressive Agents / therapeutic use
  • Inhalation Exposure / adverse effects*
  • Male
  • Middle Aged
  • Plasma Exchange
  • Retrospective Studies
  • Risk Factors
  • Skin Tests
  • Steroids
  • Vasculitis, Leukocytoclastic, Cutaneous / diagnosis
  • Vasculitis, Leukocytoclastic, Cutaneous / etiology*
  • Vasculitis, Leukocytoclastic, Cutaneous / therapy
  • Vehicle Emissions / adverse effects*

Substances

  • Anti-Inflammatory Agents
  • Antigens
  • Dust
  • Immunosuppressive Agents
  • Steroids
  • Vehicle Emissions
  • Cyclophosphamide