Chlorzoxazone or 1-EBIO increases Na(+) absorption across cystic fibrosis airway epithelial cells

Am J Physiol Lung Cell Mol Physiol. 2001 Nov;281(5):L1123-9. doi: 10.1152/ajplung.2001.281.5.L1123.

Abstract

Previous studies demonstrated that chlorzoxazone or 1-ethyl-2-benzimidazolinone (1-EBIO) enhances transepithelial Cl(-) secretion by increasing basolateral K(+) conductance (G(K)) (Singh AK, Devor DC, Gerlach AC, Gondor M, Pilewski JM, and Bridges RJ. J Pharmacol Exp Ther 292: 778-787, 2000). Hence these compounds may be useful to treat cystic fibrosis (CF) airway disease. The goal of the present study was to determine whether chlorzoxazone or 1-EBIO altered ion transport across Delta F508-CF transmembrane conductance regulator homozygous CFT1 airway cells. CFT1 monolayers exhibited a basal short-circuit current that was abolished by apical amiloride (inhibition constant 320 nM) as expected for Na(+) absorption. The addition of chlorzoxazone (400 microM) or 1-EBIO (2 mM) increased the amiloride-sensitive I(sc) approximately 2.5-fold. This overlapping specificity may preclude use of these compounds as CF therapeutics. Assaying for changes in the basolateral G(K) with a K(+) gradient plus the pore-forming antibiotic amphotericin B revealed that chlorzoxazone or 1-EBIO evoked an approximately 10-fold increase in clotrimazole-sensitive G(K). In contrast, chlorzoxazone did not alter epithelial Na(+) channel-mediated currents across basolateral-permeabilized monolayers or in Xenopus oocytes. These data further suggest that alterations in basolateral G(K) alone can modulate epithelial Na(+) transport.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Amiloride / pharmacology
  • Animals
  • Benzimidazoles / pharmacology*
  • Calcium Channel Agonists / pharmacology
  • Cell Polarity
  • Cells, Cultured
  • Chlorides / metabolism
  • Chlorzoxazone / pharmacology*
  • Cystic Fibrosis / metabolism*
  • Cystic Fibrosis Transmembrane Conductance Regulator / genetics
  • Cystic Fibrosis Transmembrane Conductance Regulator / metabolism
  • Diuretics / pharmacology
  • Dose-Response Relationship, Drug
  • Epithelial Cells / drug effects
  • Epithelial Cells / metabolism
  • Epithelial Sodium Channels
  • Humans
  • Ion Transport
  • Muscle Relaxants, Central / pharmacology
  • Oocytes / physiology
  • Patch-Clamp Techniques
  • Potassium / metabolism
  • Respiratory Mucosa / cytology
  • Respiratory Mucosa / metabolism
  • Sodium / metabolism*
  • Sodium Channels / genetics
  • Sodium Channels / metabolism
  • Xenopus laevis / physiology

Substances

  • Benzimidazoles
  • CFTR protein, human
  • Calcium Channel Agonists
  • Chlorides
  • Diuretics
  • Epithelial Sodium Channels
  • Muscle Relaxants, Central
  • Sodium Channels
  • Cystic Fibrosis Transmembrane Conductance Regulator
  • Amiloride
  • Sodium
  • Chlorzoxazone
  • 1-ethyl-2-benzimidazolinone
  • Potassium