Effects of the Bcr/abl kinase inhibitors STI571 and adaphostin (NSC 680410) on chronic myelogenous leukemia cells in vitro

Blood. 2002 Jan 15;99(2):664-71. doi: 10.1182/blood.v99.2.664.

Abstract

The adenosine triphosphate binding-site-directed agent STI571 and the tyrphostin adaphostin are undergoing evaluation as bcr/abl kinase inhibitors. The current study compared the effects of these agents on the survival of K562 cells, bcr/abl-transduced FDC-P1 cells, and myeloid progenitors from patients with chronic myelogenous leukemia (CML) compared with healthy donors. Treatment of K562 cells with 10 microM adaphostin resulted in decreased p210(bcr/abl) polypeptide levels in the first 6 hours, followed by caspase activation and accumulation of apoptotic cells in less than 12 hours. By 24 hours, 90% of the cells were apoptotic and unable to form colonies. In contrast, 20 microM STI571 caused rapid inhibition of bcr/abl autophosphorylation without p210(bcr/abl) degradation. Although this was followed by the inhibition of Stat5 phosphorylation and the down-regulation of Bcl-x(L) and Mcl-1, only 7% +/- 3% and 25% +/- 9% of cells were apoptotic at 16 and 24 hours, respectively. Instead, the cytotoxic effects of STI571 became more pronounced with prolonged exposure, with IC90 values greater than 20 microM and 1.0 +/- 0.6 microM after 24 and 48 hours, respectively. Consistent with these results, 24-hour adaphostin exposure inhibited CML granulocyte colony-forming units (CFU-G) (median IC50, 12 microM) but not normal CFU-G (median IC50, greater than 20 microM), whereas 24-hour STI571 treatment had no effect on CML or normal CFU-G. Additional experiments revealed that STI571-resistant K562 cells remained sensitive to adaphostin. Moreover, the combination of STI571 + adaphostin induced more cytotoxicity in K562 cells and in CML CFU-G than either agent alone did. Collectively, these results identify adaphostin as a mechanistically distinct CML-selective agent that retains activity in STI571-resistant cell lines.

Publication types

  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Adamantane / analogs & derivatives
  • Adamantane / pharmacology*
  • Apoptosis / drug effects
  • Benzamides
  • Caspase 9
  • Caspases / genetics
  • Caspases / metabolism
  • Drug Synergism
  • Enzyme Induction
  • Enzyme Inhibitors / pharmacology*
  • Fusion Proteins, bcr-abl / antagonists & inhibitors*
  • Fusion Proteins, bcr-abl / biosynthesis
  • Fusion Proteins, bcr-abl / genetics
  • Humans
  • Hydroquinones / pharmacology*
  • Imatinib Mesylate
  • K562 Cells / drug effects*
  • K562 Cells / enzymology
  • Leukemia, Myelogenous, Chronic, BCR-ABL Positive / enzymology
  • Leukemia, Myelogenous, Chronic, BCR-ABL Positive / genetics
  • Leukemia, Myelogenous, Chronic, BCR-ABL Positive / pathology*
  • Phosphorylation / drug effects
  • Piperazines / pharmacology*
  • Protein Biosynthesis
  • Protein Processing, Post-Translational / drug effects
  • Proteins / genetics
  • Pyrimidines / pharmacology*
  • Recombinant Fusion Proteins / physiology
  • Serpins / genetics
  • Serpins / metabolism
  • Transfection
  • Tumor Cells, Cultured / drug effects
  • Tumor Stem Cell Assay
  • Viral Proteins*
  • X-Linked Inhibitor of Apoptosis Protein

Substances

  • Benzamides
  • Enzyme Inhibitors
  • Hydroquinones
  • NSC 680410
  • Piperazines
  • Proteins
  • Pyrimidines
  • Recombinant Fusion Proteins
  • Serpins
  • Viral Proteins
  • X-Linked Inhibitor of Apoptosis Protein
  • XIAP protein, human
  • Imatinib Mesylate
  • interleukin-1beta-converting enzyme inhibitor
  • Fusion Proteins, bcr-abl
  • CASP9 protein, human
  • Caspase 9
  • Caspases
  • Adamantane