A 9-year-old boy with nephrotic syndrome who had a history of atopic dermatitis since 5 years of age is presented in this report. Generalized edema and hyperpigmented and desquamated pruritic lesions were detected on the trunk and extremities. Mesangial C1q deposition was seen on kidney biopsy. A high serum IgE level was also detected. Complete remission was achieved with steroid therapy.