Molecular genetics of male infertility: stem cell factor/c-kit system

Am J Reprod Immunol. 2002 Jul;48(1):27-33. doi: 10.1034/j.1600-0897.2002.01095.x.

Abstract

Problem: Infertility, affects about 5% of human males and genetic factors are recognized in approximately 30% of them. The mouse represents a good model to study autosomal genes that might play a role in spermatogenesis. In mice, mutations in the c-kit gene and in the gene encoding stem cell factor (SCF) cause pleiotropic defects among which sterility. A possible involvement of the SCF/c-kit system in human spermatogenesis was investigated.

Methods of study: A group of 65 idiopathic azoospermic patients was screened for the presence of mutations in the human c-kit gene codon encoding tyrosine 721 (Y721), analogous to Y719 in the murine c-kit gene (a residue known to be essential for a normal spermatogonial proliferation). Furthermore we have used a mouse model for studying the molecular mechanisms that regulate the transcription of the endogenous SCF gene.

Results: No mutations have been detected on codon encoding Y721 of the human c-kit gene, in our group of infertile patients.

Conclusions: A larger group of azoospermic patients, including preferentially patients affected by Sertoli-cell-only syndrome, should be screened in order to exclude a role of c-kit mutations in Y721 in spermatogenesis defects. In this study we also show that the murine SCF promoter is transcriptionally active and stimulated by follicle stimulating hormone (FSH), 3'-5' cyclic adenosine monophosphate (cAMP) analogs, and IBMX in primary mouse Sertoli cells, and that the cAMP effect is cell-specific, as the SCF promoter is not stimulated in other SCF-expressing cell types tested.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Cyclic AMP / metabolism
  • Humans
  • Infertility, Male / genetics*
  • Male
  • Mice
  • Mutation
  • Promoter Regions, Genetic
  • Proto-Oncogene Proteins c-kit / genetics*
  • Proto-Oncogene Proteins c-kit / metabolism
  • Sertoli Cells / metabolism
  • Spermatogenesis / physiology
  • Spermatogonia / physiology
  • Stem Cell Factor / genetics*
  • Stem Cell Factor / metabolism

Substances

  • Stem Cell Factor
  • Cyclic AMP
  • Proto-Oncogene Proteins c-kit