Granzyme B activates procaspase-3 which signals a mitochondrial amplification loop for maximal apoptosis

J Cell Biol. 2003 Mar 17;160(6):875-85. doi: 10.1083/jcb.200210158. Epub 2003 Mar 10.

Abstract

Granzyme B (GrB), acting similar to an apical caspase, efficiently activates a proteolytic cascade after intracellular delivery by perforin. Studies here were designed to learn whether the physiologic effector, GrB-serglycin, initiates apoptosis primarily through caspase-3 or through BH3-only proteins with subsequent mitochondrial permeabilization and apoptosis. Using four separate cell lines that were either genetically lacking the zymogen or rendered deficient in active caspase-3, we measured apoptotic indices within whole cells (active caspase-3, mitochondrial depolarization [DeltaPsim] and TUNEL). Adhering to these conditions, the following were observed in targets after GrB delivery: (a) procaspase-3-deficient cells fail to display a reduced DeltaPsim and DNA fragmentation; (b) Bax/Bak is required for optimal DeltaPsim reduction, caspase-3 activation, and DNA fragmentation, whereas BID cleavage is undetected by immunoblot; (c) Bcl-2 inhibits GrB-mediated apoptosis (reduced DeltaPsim and TUNEL reactivity) by blocking oligomerization of caspase-3; and (d) in procaspase-3-deficient cells a mitochondrial-independent pathway was identified which involved procaspase-7 activation, PARP cleavage, and nuclear condensation. The data therefore support the existence of a fully implemented apoptotic pathway initiated by GrB, propagated by caspase-3, and perpetuated by a mitochondrial amplification loop but also emphasize the presence of an ancillary caspase-dependent, mitochondria-independent pathway.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Animals
  • Apoptosis / physiology*
  • BH3 Interacting Domain Death Agonist Protein
  • Carrier Proteins / genetics
  • Carrier Proteins / metabolism
  • Caspase 3
  • Caspase 7
  • Caspases / deficiency*
  • Caspases / genetics
  • Caspases / metabolism
  • DNA Fragmentation / physiology
  • Enzyme Precursors / deficiency*
  • Enzyme Precursors / genetics
  • Enzyme Precursors / metabolism
  • Fibroblasts
  • Granzymes
  • Humans
  • Jurkat Cells
  • Membrane Potentials / physiology
  • Mice
  • Mitochondria / enzymology*
  • Proto-Oncogene Proteins / genetics
  • Proto-Oncogene Proteins / metabolism
  • Proto-Oncogene Proteins c-bcl-2 / genetics
  • Proto-Oncogene Proteins c-bcl-2 / metabolism
  • Serine Endopeptidases / deficiency*
  • Serine Endopeptidases / genetics
  • Signal Transduction / physiology
  • T-Lymphocytes, Cytotoxic / cytology
  • T-Lymphocytes, Cytotoxic / enzymology*
  • bcl-2-Associated X Protein

Substances

  • BAX protein, human
  • BH3 Interacting Domain Death Agonist Protein
  • BID protein, human
  • Bax protein, mouse
  • Bid protein, mouse
  • Carrier Proteins
  • Enzyme Precursors
  • Proto-Oncogene Proteins
  • Proto-Oncogene Proteins c-bcl-2
  • bcl-2-Associated X Protein
  • GZMB protein, human
  • Granzymes
  • Gzmb protein, mouse
  • Serine Endopeptidases
  • CASP3 protein, human
  • CASP7 protein, human
  • Casp3 protein, mouse
  • Casp7 protein, mouse
  • Caspase 3
  • Caspase 7
  • Caspases