Primary bilateral adrenal intravascular large B-cell lymphoma associated with adrenal failure

Intern Med. 2003 Jul;42(7):609-14. doi: 10.2169/internalmedicine.42.609.

Abstract

We report a rare case of bilateral primary adrenal non-Hodgkin's lymphoma with adrenal failure. A 66-year-old woman developed symptoms of adrenal failure. The cause of adrenal failure was suspected to be malignant lymphoma based on the high levels of serum soluble interleukin-2 receptor and LDH. Bilateral adrenalectomy was performed and pathological examination showed intravascular large B-cell lymphoma (IVL). Although complete remission was achieved, recurrence occurred three months later with brain metastases. IVL should be suspected in patients with bilateral adrenal tumors who present with rapidly progressive adrenal failure.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Adrenal Gland Neoplasms / complications*
  • Adrenal Gland Neoplasms / diagnosis
  • Adrenal Glands / blood supply
  • Adrenal Insufficiency / etiology*
  • Female
  • Humans
  • Lymphoma, B-Cell / complications*
  • Lymphoma, B-Cell / diagnosis
  • Lymphoma, Large B-Cell, Diffuse / complications*
  • Lymphoma, Large B-Cell, Diffuse / diagnosis
  • Middle Aged
  • Vascular Neoplasms / diagnosis