Electrical alternans in long QT syndrome resembling a Brugada syndrome pattern

Pacing Clin Electrophysiol. 2003 Oct;26(10):2033-5. doi: 10.1046/j.1460-9592.2003.00313.x.

Abstract

Isolated T wave alternans (repolarization alternans) is frequently associated with long QT syndrome. However, electrical alternans involving the P wave, QRS complex, ST segment (depolarization alternans), and the T wave is a rare finding. This report describes a 62-year-old woman with long QT syndrome and an electrical alternans occurring after previous syncope. Alternating QRS complexes showed a prolonged PR interval, a Brugada syndrome resembling pattern of the QRS complexes (elevation and downslope of the ST segments), and a T wave alternans. A genetic basis for the long QT syndrome has been ruled out by sequencing of all coding areas of the LQT genes. Potential mechanisms for the electrical alternans are discussed.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Bundle-Branch Block / complications
  • Bundle-Branch Block / diagnosis*
  • Bundle-Branch Block / genetics
  • Bundle-Branch Block / physiopathology
  • Diagnosis, Differential
  • Electrocardiography
  • Female
  • Heart Conduction System / physiopathology*
  • Humans
  • Long QT Syndrome / complications
  • Long QT Syndrome / diagnosis*
  • Long QT Syndrome / genetics
  • Long QT Syndrome / physiopathology
  • Middle Aged
  • Syncope / etiology