Amyloid beta protein toxicity mediated by the formation of amyloid-beta protein precursor complexes

Ann Neurol. 2003 Dec;54(6):781-9. doi: 10.1002/ana.10761.

Abstract

The amyloid-beta protein precursor, a type 1 transmembrane protein, gives rise to the amyloid beta-protein, a neurotoxic peptide postulated to be involved in the pathogenesis of Alzheimer's disease. Here, we show that soluble amyloid beta protein accelerates amyloid precursor protein complex formation, a process that contributes to neuronal cell death. The mechanism of cell death involves the recruitment of caspase-8 to the complex, followed by intracytoplasmic caspase cleavage of amyloid precursor protein. In vivo, the levels of soluble amyloid beta protein correlated with caspase-cleaved fragments of the amyloid precursor protein in brains of Alzheimer's disease subjects. These findings suggest that soluble amyloid beta protein-induced multimerization of the amyloid precursor protein may be another mechanism by which amyloid beta protein contributes to synapse loss and neuronal cell death seen in Alzheimer's disease.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Amyloid beta-Peptides / genetics
  • Amyloid beta-Peptides / metabolism
  • Amyloid beta-Peptides / toxicity
  • Amyloid beta-Protein Precursor / genetics
  • Amyloid beta-Protein Precursor / metabolism*
  • Amyloid beta-Protein Precursor / toxicity*
  • Animals
  • Brain / enzymology
  • Brain / pathology
  • Caspases / metabolism
  • Cell Death / genetics
  • Cell Line, Tumor
  • Humans
  • Mice

Substances

  • Amyloid beta-Peptides
  • Amyloid beta-Protein Precursor
  • Caspases