Two cases of tetrasomy 9p syndrome with tissue limited mosaicism

Am J Med Genet A. 2004 Feb 1;124A(4):402-6. doi: 10.1002/ajmg.a.20447.

Abstract

Tetrasomy of short arm of chromosome 9 constitutes a clinically recognizable chromosomal syndrome. Isochromosome 9p shows a strong propensity to tissue-limited mosaicism. It occurs predominantly in peripheral blood cultures, often at a lower frequency or even absent in skin, amniotic fluid or chorionic villous cell cultures. Tissue-limited nature of mosaicism may render prenatal detection of this condition very difficult. Herein, we report two new cases of mosaic tetrasomy 9p. Conventional cytogenetics (CC) and FISH studies demonstrated a differential expression of the mosaicism in several tissues. We review the literature and discuss the implications of these findings in cytogenetic prenatal diagnosis.

Publication types

  • Case Reports

MeSH terms

  • Aneuploidy*
  • Child, Preschool
  • Chromosome Disorders / diagnosis*
  • Chromosome Disorders / genetics
  • Chromosomes, Human, Pair 9*
  • Cytogenetic Analysis
  • Female
  • Humans
  • In Situ Hybridization, Fluorescence
  • Isochromosomes / genetics
  • Male
  • Mosaicism / genetics*
  • Mosaicism / pathology
  • Prenatal Diagnosis
  • Syndrome