Cholesterol 7alpha-hydroxylase deficiency in mice on an APOE*3-Leiden background impairs very-low-density lipoprotein production

Arterioscler Thromb Vasc Biol. 2004 Apr;24(4):768-74. doi: 10.1161/01.ATV.0000121572.21122.59. Epub 2004 Feb 12.

Abstract

Objective: Cholesterol 7alpha-hydroxylase (cyp7a1) catalyzes the rate-limiting step in conversion of cholesterol to bile acids. To study the relationship between bile acid biosynthesis and triglyceride metabolism, we cross-bred mice lacking cyp7a1 on a hyperlipidemic APOE*3-Leiden background.

Methods and results: Female mice received a chow or lipogenic diet. On both diets, fecal bile acid excretion was 70% decreased concomitantly with a 2-fold increased neutral sterol output. The differences in bile acid biosynthesis did not change plasma cholesterol levels. However, plasma triglyceride levels decreased by 41% and 38% in the cyp7a1-/-. APOE*3-Leiden mice as compared with APOE*3-Leiden mice on chow and lipogenic diet, respectively. Mechanistic studies showed that very-low-density lipoprotein (VLDL)-apolipoprotein B and VLDL-triglyceride production rates were reduced in cyp7a1-/-. APOE*3-Leiden mice as compared with APOE*3-Leiden mice (-34% and -35%, respectively). Cyp7a1 deficiency also increased the hepatic cholesteryl ester and triglyceride content (2.8-fold and 2.5-fold, respectively). In addition, hepatic anti-oxidative vitamin content, which can influence VLDL-production, was lower. Hepatic mRNA analysis showed decreased expression of genes involved in lipogenesis including srebf1.

Conclusions: Cyp7a1 deficiency in APOE*3-Leiden mice decreases the VLDL particle production rate, as a consequence of a strongly reduced bile acid biosynthesis, leading to a decrease in plasma triglycerides. These data underscore the close relationship between bile acid biosynthesis and triglyceride levels.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Acyltransferases / metabolism
  • Animals
  • Apolipoprotein E3
  • Apolipoproteins B / metabolism
  • Apolipoproteins E / genetics*
  • Bile Acids and Salts / metabolism*
  • Cholesterol 7-alpha-Hydroxylase / deficiency*
  • Cholesterol 7-alpha-Hydroxylase / genetics
  • Cholesterol 7-alpha-Hydroxylase / physiology
  • Cholesterol Esters / metabolism
  • Crosses, Genetic
  • Diacylglycerol O-Acyltransferase
  • Diet, Atherogenic
  • Feces
  • Female
  • Hyperlipoproteinemia Type III / genetics
  • Hyperlipoproteinemia Type III / metabolism
  • Ketone Bodies / metabolism
  • Lipid Metabolism*
  • Lipolysis
  • Lipoproteins, VLDL / biosynthesis*
  • Lipoproteins, VLDL / blood
  • Liver / metabolism
  • Male
  • Mice
  • Mice, Knockout
  • RNA, Messenger / biosynthesis
  • Sterols / metabolism
  • Triglycerides / metabolism
  • Vitamin A / metabolism
  • Vitamin E / metabolism

Substances

  • Apolipoprotein E3
  • Apolipoproteins B
  • Apolipoproteins E
  • Bile Acids and Salts
  • Cholesterol Esters
  • Ketone Bodies
  • Lipoproteins, VLDL
  • RNA, Messenger
  • Sterols
  • Triglycerides
  • apolipoprotein E3 (Leidein)
  • Vitamin A
  • Vitamin E
  • Cholesterol 7-alpha-Hydroxylase
  • Acyltransferases
  • Dgat1 protein, mouse
  • Diacylglycerol O-Acyltransferase