A B cell receptor with two Igalpha cytoplasmic domains supports development of mature but anergic B cells

J Exp Med. 2004 Mar 15;199(6):855-65. doi: 10.1084/jem.20031140.

Abstract

B cell receptor (BCR) signaling is mediated through immunoglobulin (Ig)alpha and Igbeta a membrane-bound heterodimer. Igalpha and Igbeta are redundant in their ability to support early B cell development, but their roles in mature B cells have not been defined. To examine the function of Igalpha-Igbeta in mature B cells in vivo we exchanged the cytoplasmic domain of Igalpha for the cytoplasmic domain of Igbeta by gene targeting (Igbetac-->alphac mice). Igbetac-->alphac B cells had lower levels of surface IgM and higher levels of BCR internalization than wild-type B cells. The mutant B cells were able to complete all stages of development and were long lived, but failed to differentiate into B1a cells. In addition, Igbetac-->alphac B cells showed decreased proliferative and Ca2+ responses to BCR stimulation in vitro, and were anergic to T-independent and -dependent antigens in vivo.

Publication types

  • Comparative Study
  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Animals
  • B-Lymphocytes / immunology*
  • B-Lymphocytes / metabolism
  • B-Lymphocytes / physiology
  • Blotting, Southern
  • Blotting, Western
  • Bone Marrow / immunology
  • Bromodeoxyuridine
  • Calcium / metabolism
  • Cell Differentiation / immunology
  • Cell Differentiation / physiology
  • Clonal Anergy / immunology
  • DNA Primers
  • Enzyme-Linked Immunosorbent Assay
  • Flow Cytometry
  • Genetic Vectors
  • Immunoglobulin G / blood
  • Immunoglobulin M / blood
  • Mice
  • Mice, Transgenic
  • Protein Structure, Tertiary / physiology
  • Receptors, Antigen, B-Cell / genetics
  • Receptors, Antigen, B-Cell / immunology
  • Receptors, Antigen, B-Cell / metabolism*
  • Signal Transduction / physiology*
  • Spleen / immunology

Substances

  • DNA Primers
  • Immunoglobulin G
  • Immunoglobulin M
  • Receptors, Antigen, B-Cell
  • Bromodeoxyuridine
  • Calcium

Grants and funding