CLIC-2 modulates cardiac ryanodine receptor Ca2+ release channels

Int J Biochem Cell Biol. 2004 Aug;36(8):1599-612. doi: 10.1016/j.biocel.2004.01.026.

Abstract

We have examined the biochemical and functional properties of the recently identified, uncharacterised CLIC-2 protein. Sequence alignments showed that CLIC-2 has a high degree of sequence similarity with CLIC-1 and some similarity to the omega class of glutathione transferases (GSTO). A homology model of CLIC-2 based on the crystal structure of CLIC-1 suggests that CLIC-2 belongs to the GST structural family but, unlike the GSTs, CLIC-2 exists as a monomer. It also has an unusual enzyme activity profile. While the CXXC active site motif is conserved between CLIC-2 and the glutaredoxins, no thiol transferase activity was detected. In contrast, low glutathione peroxidase activity was recorded. CLIC-2 was found to be widely distributed in tissues including heart and skeletal muscle. Functional studies showed that CLIC-2 inhibited cardiac ryanodine receptor Ca2+ release channels in lipid bilayers when added to the cytoplasmic side of the channels and inhibited Ca2+ release from cardiac sarcoplasmic reticulum vesicles. The inhibition of RyR channels was reversed by removing CLIC-2 from the solution or by adding an anti-CLIC-2 antibody. The results suggest that one function of CLIC-2 might be to limit Ca2+ release from internal stores in cells.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Binding Sites
  • Calcium / metabolism
  • Calcium Channel Blockers*
  • Chloride Channels / physiology*
  • Conserved Sequence
  • Cytoplasm / metabolism
  • Glutathione Transferase
  • Humans
  • Muscle, Skeletal / chemistry
  • Myocardium / chemistry*
  • Myocardium / metabolism
  • Ryanodine Receptor Calcium Release Channel / metabolism*
  • Sequence Alignment
  • Tissue Distribution

Substances

  • CLIC2 protein, human
  • Calcium Channel Blockers
  • Chloride Channels
  • Ryanodine Receptor Calcium Release Channel
  • Glutathione Transferase
  • Calcium