Linker for activation of B cells: a functional equivalent of a mutant linker for activation of T cells deficient in phospholipase C-gamma1 binding

J Immunol. 2004 Jun 1;172(11):6810-9. doi: 10.4049/jimmunol.172.11.6810.

Abstract

Adaptor proteins have important functions in coupling stimulation through immunoreceptors with downstream events. The adaptor linker for activation of B cells (LAB)/non-T cell activation linker (NTAL) is expressed in various immune cell types and has a similar domain structure as linker for activation of T cells (LAT). In this study we generated a LAB transgenic mouse to compare the functional differences between LAB and LAT. A LAB transgene expressed in LAT-deficient T cells was able to restore T cell development. However, these mice developed severe organomegaly with disorganized lymphoid tissues. Lymphocytes from these transgenic mice were hyperactivated, and T cells produced large amounts of type II cytokines. In addition, these activities appeared to be uncoupled from the TCR. An examination of the signaling capabilities of these T cells revealed that LAB resembled a LAT molecule unable to bind phospholipase C-gamma1.

Publication types

  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Adaptor Proteins, Signal Transducing*
  • Animals
  • B-Lymphocytes / immunology*
  • CD5 Antigens / analysis
  • Carrier Proteins / physiology*
  • Humans
  • Jurkat Cells
  • Lymphocyte Activation
  • Membrane Proteins / physiology*
  • Mice
  • Mice, Transgenic
  • Phospholipase C gamma
  • Phosphoproteins / physiology*
  • Receptors, Antigen, T-Cell / metabolism
  • T-Lymphocytes / immunology*
  • Type C Phospholipases / metabolism*

Substances

  • Adaptor Proteins, Signal Transducing
  • CD5 Antigens
  • Carrier Proteins
  • LAT protein, human
  • Lat protein, mouse
  • Membrane Proteins
  • Phosphoproteins
  • Receptors, Antigen, T-Cell
  • Type C Phospholipases
  • Phospholipase C gamma