High prevalence of coeliac disease in siblings of children with type 1 diabetes

Eur J Pediatr. 2005 Jan;164(1):9-12. doi: 10.1007/s00431-004-1547-1. Epub 2004 Oct 7.

Abstract

Coeliac disease has been shown to occur more frequently among first-degree relatives of diabetic patients than in the general population. Our objective was to assess the prevalence of endomysium antibodies (EMA) in non-diabetic siblings of Czech diabetic children and to evaluate the effects of HLA-DQ polymorphisms in determining the genetic susceptibility to coeliac disease (CD) in these subjects. We investigated 240 siblings of diabetic children from 213 families (125 males and 115 females, aged 12.6+/-4.9 years, mean +/- SD). All subjects were tested for the total IgA level to exclude IgA deficiency, and for endomysium IgA to disclose CD. In five IgA-deficient subjects, anti-gliadin IgG was used instead. Small bowel biopsy was offered to subjects with confirmed positive EMA. The HLA-DQA1, -DQB1 genotypes were determined using PCR-SSP. Positive EMA were found in 9/240 (3.8%) subjects (three males, six females). The biopsy confirmed CD in six children, two had a normal mucosal finding and one refused the biopsy. The HLA-DQ2 polymorphism was more frequent among siblings with EMA (seven of nine) than in siblings without EMA (33%), corrected P = 0.031.

Conclusion: The 3.8% frequency of coeliac disease found in siblings of diabetic children is close to the 4.3% found previously in Czech children with type 1 diabetes mellitus and is substantially higher than the rate in the healthy children population.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Antibodies, Anti-Idiotypic / blood
  • Biopsy
  • Celiac Disease / complications*
  • Celiac Disease / genetics
  • Celiac Disease / immunology
  • Child
  • Child, Preschool
  • Czech Republic
  • Diabetes Mellitus, Type 1 / complications*
  • Female
  • HLA-DQ Antigens / analysis
  • HLA-DQ alpha-Chains
  • HLA-DQ beta-Chains
  • Humans
  • Immunoglobulin A / blood
  • Male
  • Prevalence
  • Siblings*

Substances

  • Antibodies, Anti-Idiotypic
  • HLA-DQ Antigens
  • HLA-DQ alpha-Chains
  • HLA-DQ beta-Chains
  • HLA-DQA1 antigen
  • HLA-DQB1 antigen
  • Immunoglobulin A