Orthostatic blood pressure control in Marfan's syndrome

Europace. 2005 Jan;7(1):25-7. doi: 10.1016/j.eupc.2004.05.009.

Abstract

A 33-year old male patient, with Marfan's syndrome, reported symptoms of orthostatic intolerance and fatigue as a longstanding problem. Orthostatic cardiovascular examination showed poor orthostatic tolerance, with a rise in heart rate and a fall in arterial blood pressure and cerebral blood flow velocity. Self-discovered physical counterpressure manoeuvers improved symptoms, related to a substantial increase in arterial pressure and cerebral perfusion. When orthostatic complaint are reported by patients with Marfan's syndrome, physical counterpressure manoeuvers should be advised to reduce symptoms of postural hypotension.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Blood Flow Velocity / physiology
  • Cerebrovascular Circulation / physiology
  • Heart Rate / physiology
  • Humans
  • Hypotension, Orthostatic / etiology
  • Hypotension, Orthostatic / physiopathology*
  • Hypotension, Orthostatic / prevention & control*
  • Male
  • Marfan Syndrome / complications*