The human prion protein alpha2 helix: a thermodynamic study of its conformational preferences

Proteins. 2005 Apr 1;59(1):72-9. doi: 10.1002/prot.20395.

Abstract

We have synthesized both free and terminally-blocked peptide corresponding to the second helical region of the globular domain of normal human prion protein, which has recently gained the attention of structural biologists because of a possible role in the nucleation process and fibrillization of prion protein. The profile of the circular dichroism spectrum of the free peptide was that typical of alpha-helix, but was converted to that of beta-structure in about 16 h. Instead, below 2.1 x 10(-5) M, the spectrum of the blocked peptide exhibited a single band centered at 200 nm, unequivocally associated to random conformations, which did not evolve even after 24 h. Conformational preferences of this last peptide have been investigated as a function of temperature, using trifluoroethanol or low-concentration sodium dodecyl sulfate as alpha- or beta-structure inducers, respectively. Extrapolation of free energy data to zero concentration of structuring agent highlighted that the peptide prefers alpha-helical to beta-type organization, in spite of results from prediction algorithms. However, the free energy difference between the two forms, as obtained by a thermodynamic cycle, is subtle (roughly 5-8 kJ mol(-1) at any temperature from 280 K to 350 K), suggesting conformational ambivalence. This result supports the view that, in the prion protein, the structural behavior of the peptide is governed by the cellular microenvironment.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Humans
  • Prions / chemistry*
  • Prions / metabolism
  • Protein Conformation*
  • Protein Structure, Secondary*
  • Sodium Dodecyl Sulfate
  • Thermodynamics

Substances

  • Prions
  • Sodium Dodecyl Sulfate