Identification of 32 novel mutations in the factor VIII gene in Indian patients with hemophilia A

Haematologica. 2005 Feb;90(2):283-4.

Abstract

Seventy-five unrelated hemophilia A patients from India were analyzed for factor VIII gene defects. Intron 22 inversion was identified in 22 patients and intron 1 inversion in 2 patients. In the remaining 51 patients without inversions screening the FVIII gene by denaturing high performance liquid chromatography (DHPLC) revealed 42 different mutations in 44 unrelated subjects. These included 14 missense, 7 nonsense, 9 splice site, 8 deletional, 3 insertional mutations and one indel mutation. Of these, 32 were novel gene alterations. The hotspots included intron 22 inversion, CpG and adenine runs.

Publication types

  • Letter
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Binding Sites
  • Chromatography, High Pressure Liquid
  • CpG Islands
  • DNA Mutational Analysis
  • Exons
  • Factor VIII / genetics*
  • Gene Deletion
  • Hemophilia A / genetics*
  • Humans
  • India
  • Introns
  • Mutation*

Substances

  • Factor VIII