Alloisoleucine in isovaleric acidaemia

J Inherit Metab Dis. 1992;15(1):154-5. doi: 10.1007/BF01800358.
No abstract available

MeSH terms

  • 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide)
  • Amino Acid Metabolism, Inborn Errors / blood*
  • Amino Acid Metabolism, Inborn Errors / diet therapy
  • Child, Preschool
  • Hemiterpenes
  • Humans
  • Infant
  • Isoleucine / blood*
  • Ketone Oxidoreductases / antagonists & inhibitors
  • Multienzyme Complexes / antagonists & inhibitors
  • Pentanoic Acids / blood*

Substances

  • Hemiterpenes
  • Multienzyme Complexes
  • Pentanoic Acids
  • Isoleucine
  • isovaleric acid
  • Ketone Oxidoreductases
  • 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide)