Risk estimation in localized unresectable single copy MYCN neuroblastoma by the status of chromosomes 1p and 11q

Cancer Lett. 2006 Jun 18;237(2):215-22. doi: 10.1016/j.canlet.2005.06.001. Epub 2005 Jul 12.

Abstract

In localized neuroblastoma, the identification of patients requiring intensive treatment is still difficult. We retrospectively analyzed data of 280 single copy MYCN stage 2 and 3 neuroblastoma patients with gross residual tumor after initial surgery. The 3-year-event free survival of the total group was 83+/-2%, and 3-year-overall survival was 92+/-2%. Patients < or=1.5 years had a better outcome than older children. Deletions/imbalances of chromosome 1p were found in 9/90 patients and were associated with a higher event rate but not with a higher death rate. Aberrations of chromosome 11q in 14/91 patients were correlated with a higher event and death rate. Multivariate analysis identified 1p aberrations as important for event free survival and 11q aberrations for overall survival.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Child
  • Child, Preschool
  • Chromosome Aberrations
  • Chromosomes, Human, Pair 1*
  • Chromosomes, Human, Pair 11*
  • Disease-Free Survival
  • Humans
  • Infant
  • Infant, Newborn
  • N-Myc Proto-Oncogene Protein
  • Neuroblastoma / genetics*
  • Neuroblastoma / metabolism
  • Neuroblastoma / therapy*
  • Nuclear Proteins / metabolism*
  • Oncogene Proteins / metabolism*
  • Retrospective Studies
  • Risk

Substances

  • MYCN protein, human
  • N-Myc Proto-Oncogene Protein
  • Nuclear Proteins
  • Oncogene Proteins