Familial aggregation, the PDE4D gene, and ischemic stroke in a genetically isolated population

Neurology. 2005 Oct 25;65(8):1203-9. doi: 10.1212/01.wnl.0000178744.42953.b7. Epub 2005 Sep 14.

Abstract

Objective: The purpose of this investigation was to study the familial aggregation of ischemic stroke and the association between the PDE4D gene and ischemic stroke.

Methods: The study was performed in an isolated population in The Netherlands, where the authors identified 91 patients with ischemic stroke. Ischemic stroke was subclassified in large- and small-vessel infarction. The authors calculated kinship and inbreeding coefficients and genotyped all patients for three single-nucleotide polymorphisms (SNPs) in the PDE4D gene.

Results: The proportion of related pairs was higher in patients with ischemic stroke (68.8%) compared with controls (30.7%; p < 0.001). For large-vessel infarction, the proportion of related pairs was higher (71%) compared with small-vessel infarction (62.8%; p < 0.001). Familial aggregation was strongest for patients with early onset (age at onset < 45 years). All stroke groups were significantly more inbred compared with controls. In inbred individuals, the C allele of SNP45 increased the risk of small-vessel infarction 4.8 times (95% CI 1.1 to 22.3) compared with controls (p = 0.04). The T allele of SNP39 increased the risk of small-vessel infarction 6.3 times (95% CI 1.4 to 28.7) compared with controls (p = 0.02). No associations were found for large-vessel stroke.

Conclusions: There was familial aggregation of ischemic stroke and a difference in degree of familial clustering between stroke subtypes. The authors also found that the PDE4D gene is significantly associated with small-vessel infarction in inbred individuals.

MeSH terms

  • 3',5'-Cyclic-AMP Phosphodiesterases / genetics*
  • Adult
  • Aged
  • Brain Ischemia / epidemiology*
  • Brain Ischemia / genetics*
  • Cerebral Arteries / pathology
  • Cerebral Arteries / physiopathology
  • Consanguinity
  • Cyclic Nucleotide Phosphodiesterases, Type 3
  • Cyclic Nucleotide Phosphodiesterases, Type 4
  • DNA Mutational Analysis
  • Family
  • Family Health
  • Female
  • Genetic Predisposition to Disease / genetics*
  • Genetic Testing
  • Genotype
  • Humans
  • Male
  • Microcirculation / pathology
  • Microcirculation / physiopathology
  • Middle Aged
  • Netherlands / epidemiology
  • Polymorphism, Single Nucleotide / genetics
  • Risk Factors
  • Stroke / epidemiology*
  • Stroke / genetics*

Substances

  • 3',5'-Cyclic-AMP Phosphodiesterases
  • Cyclic Nucleotide Phosphodiesterases, Type 3
  • Cyclic Nucleotide Phosphodiesterases, Type 4
  • PDE4D protein, human