The prognostic value of MLL-AF9 detection in patients with t(9;11)(p22;q23)-positive acute myeloid leukemia

Haematologica. 2005 Dec;90(12):1626-34.

Abstract

Background and objectives: Translocation (9;11) is the most common t(11q23) in acute myeloid leukemia (AML). A considerable number of patients with this cytogenetic abnormality relapse and die of their disease. We evaluated the clinical significance of minimal residual disease (MRD) monitoring in t(9;11)(p22;q23)-positive AML patients using real-time quantitative reverse transcriptase polymerase chain reaction (RQ-PCR) analysis.

Design and methods: We identified 34 newly diagnosed patients with t(9;11)(p22;q23)-positive AML treated within three multicenter trials of the AML Study Group. MRD could be investigated by RQ-PCR in 19 patients during and after therapy. Because of the relatively low sensitivity of the RQ-PCR (10(-3) to 10(-4) at the cellular level), samples from RQ-PCR-negative patients were also analyzed by nested polymerase chain reaction (nPCR; sensitivity 10-4 to 10-5 at the cellular level).

Results: RQ-PCR monitoring revealed two groups of patients: group 1 (n=11) had negative RQ-PCR in all samples collected in hematologic complete remission whereas group 2 (n=8) had at least one positive RQ-PCR in samples collected in complete remission during therapy. Group 1 had a significantly lower cumulative incidence of relapse (p=0.004) and better overall survival (p=0.003) compared to group 2. nPCR did not add information to that gained from RQ-PCR. Molecular relapse was detected in two patients by RQ-PCR four and six weeks, respectively before hematologic relapse occurred. Quantitative MLL-AF9 levels at diagnosis or during and after therapy had no prognostic impact.

Interpretation and conclusions: Early achievement of sustained RQ-PCR negativity appears to be a prerequisite for long-term hematologic complete remission in t(9;11)-positive AML. Furthermore, RQ-PCR might be useful for early detection of relapse. Additional patients need to be studied to corroborate these findings.

Publication types

  • Comparative Study
  • Evaluation Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Antineoplastic Combined Chemotherapy Protocols / administration & dosage
  • Antineoplastic Combined Chemotherapy Protocols / therapeutic use
  • Biomarkers, Tumor / blood*
  • Chromosomes, Human, Pair 11 / genetics*
  • Chromosomes, Human, Pair 11 / ultrastructure
  • Chromosomes, Human, Pair 9 / genetics*
  • Chromosomes, Human, Pair 9 / ultrastructure
  • Cohort Studies
  • Combined Modality Therapy
  • Cytarabine / administration & dosage
  • Etoposide / administration & dosage
  • Humans
  • Idarubicin / administration & dosage
  • Leukemia, Myeloid / blood
  • Leukemia, Myeloid / drug therapy
  • Leukemia, Myeloid / genetics
  • Leukemia, Myeloid / mortality
  • Leukemia, Myeloid / pathology*
  • Leukemia, Myeloid / surgery
  • Middle Aged
  • Mitoxantrone / administration & dosage
  • Multicenter Studies as Topic
  • Myeloid-Lymphoid Leukemia Protein / blood*
  • Neoplasm, Residual
  • Oncogene Proteins, Fusion / blood*
  • Peripheral Blood Stem Cell Transplantation
  • Polymerase Chain Reaction / methods
  • Prognosis
  • Randomized Controlled Trials as Topic
  • Recurrence
  • Remission Induction
  • Survival Analysis
  • Translocation, Genetic*
  • Treatment Outcome
  • Tretinoin / administration & dosage

Substances

  • Biomarkers, Tumor
  • MLL-AF9 fusion protein, human
  • Oncogene Proteins, Fusion
  • Cytarabine
  • Myeloid-Lymphoid Leukemia Protein
  • Tretinoin
  • Etoposide
  • Mitoxantrone
  • Idarubicin

Supplementary concepts

  • ICE protocol 4
  • MAC chemotherapy protocol