The alpha-synuclein gene in multiple system atrophy

J Neurol Neurosurg Psychiatry. 2006 Apr;77(4):464-7. doi: 10.1136/jnnp.2005.073528.

Abstract

Background: The formation of alpha-synuclein aggregates may be a critical event in the pathogenesis of multiple system atrophy (MSA). However, the role of this gene in the aetiology of MSA is unknown and untested.

Method: The linkage disequilibrium (LD) structure of the alpha-synuclein gene was established and LD patterns were used to identify a set of tagging single nucleotide polymorphisms (SNPs) that represent 95% of the haplotype diversity across the entire gene. The effect of polymorphisms on the pathological expression of MSA in pathologically confirmed cases was also evaluated.

Results and conclusion: In 253 Gilman probable or definite MSA patients, 457 possible, probable, and definite MSA cases and 1472 controls, a frequency difference for the individual tagging SNPs or tag-defined haplotypes was not detected. No effect was observed of polymorphisms on the pathological expression of MSA in pathologically confirmed cases.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Gene Expression / genetics
  • Genotype
  • Haplotypes / genetics
  • Humans
  • Linkage Disequilibrium / genetics
  • Multiple System Atrophy / metabolism*
  • Multiple System Atrophy / pathology*
  • Polymorphism, Single Nucleotide / genetics
  • Sequence Tagged Sites
  • alpha-Synuclein / genetics*

Substances

  • alpha-Synuclein