Human cardiac myosin autoantibodies impair myocyte contractility: a cause-and-effect relationship

FASEB J. 2006 Apr;20(6):651-60. doi: 10.1096/fj.04-3001com.

Abstract

The functional relevance of autoantibodies (Abs) against cardiac myosin (CM) in clinical idiopathic dilated cardiomyopathy (DCM) remains controversial. The study sought to determine effects of human Abs affinity-purified (AF) by immunoaffinity column chromotography on excitation-contraction coupling in isolated myocytes. Effects of CM-Abs from heart failure patients with DCM (n=19) and ischemic heart disease (IHD, n=19) on contractility, L-type Ca2+ current, and Ca2+ transients in continuously perfused rat ventricular myocytes were studied. Immunofluorescence studies using confocal microscopy were carried out to determine whether Abs were internalized. AF-Abs from either group did not differ in IgG titer but differed in their elution profiles. The IgG3 subclass response was higher in AF fractions from DCM (21%) than IHD (5%) patients. The Abs reduced the capacity of field-stimulated myocytes to contract in a dose-dependent manner. Inhibition of contraction, as a percentage of untreated cells, was greater with DCM than IHD-Abs (P=0.004), and the effect was independent of Ab titer. An increase in frequency of the beating myocytes (0.2 to 3.0 Hz) raised peak systolic and diastolic levels of [Ca2+]i of cells treated with DCM but not IHD-Abs (P<0.005). The AF-Abs were not internalized by myocytes and had no effect on L-type Ca2+ currents. The altered sensitivity of the myofilaments to [Ca2+]i by CM-Abs may represent a potential mechanism of autoantibody-mediated impairment in clinical DCM.

MeSH terms

  • Adult
  • Animals
  • Autoantibodies / immunology*
  • Autoantibodies / pharmacology*
  • Calcium / metabolism
  • Cardiac Myosins / immunology*
  • Cardiomyopathy, Dilated / immunology
  • Cells, Cultured
  • Female
  • Humans
  • Male
  • Middle Aged
  • Muscle Cells / cytology
  • Muscle Cells / metabolism*
  • Muscle Contraction / drug effects*
  • Myocardial Ischemia / immunology
  • Rats

Substances

  • Autoantibodies
  • Cardiac Myosins
  • Calcium