HCV-NS3 and IgG-Fc crossreactive IgM in patients with type II mixed cryoglobulinemia and B-cell clonal proliferations

Leukemia. 2006 Jun;20(6):1145-54. doi: 10.1038/sj.leu.2404201.

Abstract

We demonstrate that in three cases of MC (two with immunocytoma), the IgM-RF+ component of their cryoprecipitated represents the circulating counterpart of the B-cell receptor (BCR) of the monoclonal overexpanded B-cell population. These IgMs were isolated and used to demonstrate a crossreactivity against both hepatitis C virus (HCV) NS3 antigen and the Fc portion of IgG. Epitopes were identified in a fraction of exemplary samples by using epitope excision approach (NS(31250-1334) and IgG Fc(345-355)). The same phenomenon of crossreactivity has been shown to occur in vivo after immunization of a mouse with the NS3(1251-1270) peptide. To verify if the same reaction was also present in MC samples characterized by an oligo/polyclonal B-cell proliferation, IgM crossreactivity was tested in 14 additional samples. Five out of the 14 were reactive against HCV NS3 and 11 out of 14 were reactive against IgG-Fc peptide. The data support the role of HCV NS3 antigen in a subset of patients with MC, whereas the high frequency of the IgG-Fc epitope suggests that these B cells originate from precursors strongly selected for auto-IgG specificity. We suggest that engagement of specific BCRs by NS3 (or NS3-immunocomplex) antigen could explain the prevalence of IgM cryoglobulins in these patients.

Publication types

  • Comparative Study
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Clone Cells
  • Cryoglobulinemia / classification*
  • Cryoglobulinemia / diagnosis
  • Cryoglobulinemia / immunology*
  • Epitopes / immunology
  • Humans
  • Immunoglobulin Fc Fragments / immunology*
  • Immunoglobulin M / drug effects
  • Immunoglobulin M / immunology*
  • Lymphoma, B-Cell / immunology*
  • Models, Molecular
  • Peptide Fragments / immunology
  • Protein Binding
  • Protein Conformation
  • Protein Structure, Secondary
  • Receptors, Antigen, B-Cell / immunology
  • Rheumatoid Factor / drug effects
  • Rheumatoid Factor / immunology
  • Viral Nonstructural Proteins / immunology*
  • Viral Nonstructural Proteins / pharmacology

Substances

  • Epitopes
  • Immunoglobulin Fc Fragments
  • Immunoglobulin M
  • NS3 protein, hepatitis C virus
  • Peptide Fragments
  • Receptors, Antigen, B-Cell
  • Viral Nonstructural Proteins
  • Rheumatoid Factor