Terminal 14q32.33 deletion: genotype-phenotype correlation

Am J Med Genet A. 2006 Nov 1;140(21):2324-9. doi: 10.1002/ajmg.a.31438.

Abstract

We report on a female infant presenting with psychomotor retardation and facial dysmorphism. Cytogenetic studies showed an abnormal chromosome 14 with ectopic NOR sequences at the extremity of the long arm with a terminal 14q32.33 deletion. Review of the eight cases with pure terminal 14q32.3 deletions described to date documented that our observation is the smallest terminal 14q deletion ever reported. Thus, genotype-phenotype correlation allows us to delimit the critical region for mental retardation, hypotonia, epi-telecanthus, short bulbous nose, long philtrum, thin upper lip, and small mouth observed in 14 qter deletions to the subtelomeric 1.6 Mb of chromosome 14.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Brain / abnormalities
  • Child, Preschool
  • Chromosome Deletion*
  • Chromosomes, Human, Pair 14 / genetics*
  • Craniofacial Abnormalities / genetics
  • Cytogenetics
  • Female
  • Genotype
  • Humans
  • In Situ Hybridization, Fluorescence
  • Infant
  • Intellectual Disability / genetics
  • Muscle Hypotonia / genetics
  • Myopia / genetics
  • Phenotype