Chaperone-mediated coupling of endoplasmic reticulum and mitochondrial Ca2+ channels

J Cell Biol. 2006 Dec 18;175(6):901-11. doi: 10.1083/jcb.200608073.

Abstract

The voltage-dependent anion channel (VDAC) of the outer mitochondrial membrane mediates metabolic flow, Ca(2+), and cell death signaling between the endoplasmic reticulum (ER) and mitochondrial networks. We demonstrate that VDAC1 is physically linked to the endoplasmic reticulum Ca(2+)-release channel inositol 1,4,5-trisphosphate receptor (IP(3)R) through the molecular chaperone glucose-regulated protein 75 (grp75). Functional interaction between the channels was shown by the recombinant expression of the ligand-binding domain of the IP(3)R on the ER or mitochondrial surface, which directly enhanced Ca(2+) accumulation in mitochondria. Knockdown of grp75 abolished the stimulatory effect, highlighting chaperone-mediated conformational coupling between the IP(3)R and the mitochondrial Ca(2+) uptake machinery. Because organelle Ca(2+) homeostasis influences fundamentally cellular functions and death signaling, the central location of grp75 may represent an important control point of cell fate and pathogenesis.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Aequorin
  • Animals
  • Calcium / metabolism*
  • Calcium Signaling
  • Endoplasmic Reticulum / metabolism*
  • HSP70 Heat-Shock Proteins / metabolism
  • HeLa Cells
  • Humans
  • Inositol 1,4,5-Trisphosphate / metabolism
  • Inositol 1,4,5-Trisphosphate Receptors / metabolism
  • Liver / metabolism
  • Membrane Proteins / metabolism
  • Mice
  • Mitochondria / metabolism*
  • Molecular Chaperones / metabolism*
  • Protein Conformation
  • Rats
  • Two-Hybrid System Techniques
  • Voltage-Dependent Anion Channel 1 / metabolism*

Substances

  • HSP70 Heat-Shock Proteins
  • Inositol 1,4,5-Trisphosphate Receptors
  • Membrane Proteins
  • Molecular Chaperones
  • VDAC1 protein, human
  • Vdac1 protein, rat
  • glucose-regulated proteins
  • Aequorin
  • Inositol 1,4,5-Trisphosphate
  • Voltage-Dependent Anion Channel 1
  • Calcium