Dynamics of alpha-synuclein aggregation and inhibition of pore-like oligomer development by beta-synuclein

FEBS J. 2007 Apr;274(7):1862-77. doi: 10.1111/j.1742-4658.2007.05733.x.

Abstract

Accumulation of alpha-synuclein resulting in the formation of oligomers and protofibrils has been linked to Parkinson's disease and Lewy body dementia. In contrast, beta-synuclein (beta-syn), a close homologue, does not aggregate and reduces alpha-synuclein (alpha-syn)-related pathology. Although considerable information is available about the conformation of alpha-syn at the initial and end stages of fibrillation, less is known about the dynamic process of alpha-syn conversion to oligomers and how interactions with antiaggregation chaperones such as beta-synuclein might occur. Molecular modeling and molecular dynamics simulations based on the micelle-derived structure of alpha-syn showed that alpha-syn homodimers can adopt nonpropagating (head-to-tail) and propagating (head-to-head) conformations. Propagating alpha-syn dimers on the membrane incorporate additional alpha-syn molecules, leading to the formation of pentamers and hexamers forming a ring-like structure. In contrast, beta-syn dimers do not propagate and block the aggregation of alpha-syn into ring-like oligomers. Under in vitro cell-free conditions, alpha-syn aggregates formed ring-like structures that were disrupted by beta-syn. Similarly, cells expressing alpha-syn displayed increased ion current activity consistent with the formation of Zn(2+)-sensitive nonselective cation channels. These results support the contention that in Parkinson's disease and Lewy body dementia, alpha-syn oligomers on the membrane might form pore-like structures, and that the beneficial effects of beta-synuclein might be related to its ability to block the formation of pore-like structures.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, Non-P.H.S.

MeSH terms

  • Cations / metabolism
  • Cell Line
  • Computer Simulation*
  • Electrophysiology
  • Humans
  • Ion Channels / metabolism
  • Microscopy, Electron, Scanning
  • Models, Molecular*
  • Phosphatidylcholines / chemistry
  • Protein Binding / drug effects
  • Protein Conformation
  • Protein Structure, Quaternary
  • Protein Structure, Secondary
  • Static Electricity
  • Transfection
  • Zinc / pharmacology
  • alpha-Synuclein / chemistry*
  • alpha-Synuclein / genetics
  • alpha-Synuclein / metabolism
  • beta-Synuclein / chemistry*
  • beta-Synuclein / genetics
  • beta-Synuclein / metabolism

Substances

  • Cations
  • Ion Channels
  • Phosphatidylcholines
  • alpha-Synuclein
  • beta-Synuclein
  • Zinc
  • 1-palmitoyl-2-oleoylphosphatidylcholine