Rare expression of BSAP (PAX-5) in mature T-cell lymphomas

Mod Pathol. 2007 Jun;20(6):632-7. doi: 10.1038/modpathol.3800778. Epub 2007 Apr 13.

Abstract

Lineage determination in lymphomas is based on the assessment of lineage-specific markers, such as the B-cell-specific activator protein of the paired box family (BSAP, PAX-5) for the B-cell lineage. BSAP is thought to be expressed exclusively in B cells from the pro-B- to the mature B-cell stage and then silenced in plasma cells. BSAP has oncogenic potential and experimental evidence shows that the T-cell lineage is prone to this effect. Herein, we report on a BSAP-positive peripheral T-cell lymphoma with monoclonal T-cell receptor gamma-gene rearrangement. To assess the relative frequency of BSAP expression in mature T-cell lymphomas, we constructed and examined a tissue microarray consisting of 43 angioimmunoblastic T-cell lymphomas and peripheral T-cell lymphomas and detected no additional BSAP-positive cases. To conclude, BSAP can probably contribute to T-cell lymphomagenesis not only in vitro, but also in vivo. It is rarely expressed in peripheral T-cell lymphoma, thus its detection on lymphoid malignancies cannot be considered definitively lineage specific.

MeSH terms

  • Aged
  • Biomarkers, Tumor / biosynthesis
  • Cell Lineage
  • Female
  • Gene Rearrangement, gamma-Chain T-Cell Antigen Receptor
  • Humans
  • Lymphoma, T-Cell / metabolism*
  • Lymphoma, T-Cell / pathology
  • Lymphoma, T-Cell, Peripheral / metabolism
  • Male
  • Middle Aged
  • PAX5 Transcription Factor / biosynthesis*
  • Tissue Array Analysis

Substances

  • Biomarkers, Tumor
  • PAX5 Transcription Factor
  • PAX5 protein, human