Stable myocardial-specific AAV6-S100A1 gene therapy results in chronic functional heart failure rescue

Circulation. 2007 May 15;115(19):2506-15. doi: 10.1161/CIRCULATIONAHA.106.671701. Epub 2007 Apr 30.

Abstract

Background: The incidence of heart failure is ever-growing, and it is urgent to develop improved treatments. An attractive approach is gene therapy; however, the clinical barrier has yet to be broken because of several issues, including the lack of an ideal vector supporting safe and long-term myocardial transgene expression.

Methods and results: Here, we show that the use of a recombinant adeno-associated viral (rAAV6) vector containing a novel cardiac-selective enhancer/promoter element can direct stable cardiac expression of a therapeutic transgene, the calcium (Ca2+)-sensing S100A1, in a rat model of heart failure. The chronic heart failure-rescuing properties of myocardial S100A1 expression, the result of improved sarcoplasmic reticulum Ca2+ handling, included improved contractile function and left ventricular remodeling. Adding to the clinical relevance, long-term S100A1 therapy had unique and additive beneficial effects over beta-adrenergic receptor blockade, a current pharmacological heart failure treatment.

Conclusions: These findings demonstrate that stable increased expression of S100A1 in the failing heart can be used for long-term reversal of LV dysfunction and remodeling. Thus, long-term, cardiac-targeted rAAV6-S100A1 gene therapy may be of potential clinical utility in human heart failure.

Publication types

  • Evaluation Study
  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Actins / genetics
  • Animals
  • Binding Sites
  • Calcium Signaling
  • Cardiomegaly / prevention & control
  • Dependovirus / genetics
  • Enhancer Elements, Genetic
  • Genes, Reporter
  • Genetic Therapy*
  • Genetic Vectors / genetics
  • Genetic Vectors / therapeutic use
  • Green Fluorescent Proteins / genetics
  • Heart Failure / etiology
  • Heart Failure / physiopathology
  • Heart Failure / therapy*
  • Heart Function Tests
  • Humans
  • Lac Operon
  • Mice
  • Mice, Inbred C57BL
  • Myocardial Contraction
  • Myocardial Infarction / complications
  • Organ Specificity
  • Promoter Regions, Genetic
  • Rats
  • Recombinant Fusion Proteins / physiology
  • S100 Proteins / genetics
  • S100 Proteins / physiology*

Substances

  • Actins
  • Recombinant Fusion Proteins
  • S100 Proteins
  • S100A1 protein
  • Green Fluorescent Proteins