Clinical and immunopathologic findings in oral lichen planus pemphigoides

Oral Surg Oral Med Oral Pathol Oral Radiol Endod. 2007 Jun;103(6):808-13. doi: 10.1016/j.tripleo.2006.03.020. Epub 2006 Sep 12.

Abstract

Lichen planus pemphigoides (LPP) is a rare, acquired, immunobullous disorder of skin that occasionally involves oral mucous membranes. Clinical, histologic, and immunopathologic findings of the oral manifestations of LPP are described. Clinical features are lichenoid striae, erosions, and ulcerations involving gingiva and buccal mucosae. Histopathologic features are similar to those of ora lichen planus. Direct immunofluorescence demonstrates linear deposits of immunoglobulin G and complement component C3 along the basement membrane with fibrillar deposits of fibrin at the epithelial/lamina propria junction. Fluorescence overlay antigen mapping and laser scanning confocal microscopy of the biopsy specimen exhibits colocalization of in situ antibodies with beta4 integrin, a marker of the keratinocyte basal plasma membrane and upper lamina lucida, consistent with the location of the bullous pemphigoid antigens. This case report describes a case of LPP that presented exclusively as an oral condition. Lichen planus pemphigoides should be considered in the clinical differential diagnosis of vesiculoerosive oral mucosal diseases.

Publication types

  • Case Reports

MeSH terms

  • Anti-Infective Agents / therapeutic use
  • Anti-Inflammatory Agents / therapeutic use
  • Chlorhexidine / analogs & derivatives
  • Chlorhexidine / therapeutic use
  • Clobetasol / administration & dosage
  • Complement C3 / analysis
  • Doxycycline / therapeutic use
  • Female
  • Fluorescent Antibody Technique / methods
  • Gingival Diseases / drug therapy
  • Gingival Diseases / immunology
  • Gingival Diseases / pathology*
  • Humans
  • Immunoglobulin G / analysis
  • Keratinocytes / chemistry
  • Keratinocytes / immunology
  • Keratinocytes / pathology
  • Lichen Planus, Oral / drug therapy
  • Lichen Planus, Oral / immunology
  • Lichen Planus, Oral / pathology*
  • Microscopy, Confocal
  • Middle Aged
  • Mouth Mucosa / chemistry
  • Mouth Mucosa / immunology
  • Mouth Mucosa / pathology
  • Ointments / therapeutic use
  • Oral Ulcer / drug therapy
  • Oral Ulcer / immunology
  • Oral Ulcer / pathology
  • Pemphigoid, Bullous / drug therapy
  • Pemphigoid, Bullous / immunology
  • Pemphigoid, Bullous / pathology*

Substances

  • Anti-Infective Agents
  • Anti-Inflammatory Agents
  • Complement C3
  • Immunoglobulin G
  • Ointments
  • Clobetasol
  • chlorhexidine gluconate
  • Doxycycline
  • Chlorhexidine