Eruptive pseudoangiomatosis: report of an adult case and unifying hypothesis of the pathogenesis of paediatric and adult cases

Dermatology. 2007;215(1):59-62. doi: 10.1159/000102035.

Abstract

One month after the onset of immunosuppressive treatment with corticosteroids and mycophenolate mofetil for a newly diagnosed pemphigus vulgaris, a 50-year-old female patient developed a new eruption clinically and histomorphologically consistent with eruptive pseudoangiomatosis (EP). Its self-limited course further confirmed this diagnosis. Although initially described as a paediatric eruption, meanwhile more adult cases of EP (30 out of a total of 53 cases identified by a Medline search) are reported in the literature. The review of adult cases of EP disclosed some common clinical and epidemiological characteristics: adult EP cases tend to cluster in the Mediterranean region of Europe, develop during the summer months, sometimes in the form of limited micro-epidemics, affect immunocompromised individuals and have lesions confined to the exposed skin sites. These characteristics, together with the exanthematic nature of the disease in children, point to some vector-transmitted infectious agent as the cause of this probably underdiagnosed disease.

Publication types

  • Case Reports
  • Review

MeSH terms

  • Angiomatosis / drug therapy
  • Angiomatosis / immunology
  • Angiomatosis / pathology*
  • Biopsy, Needle
  • Child, Preschool
  • Drug Therapy, Combination
  • Female
  • Follow-Up Studies
  • Humans
  • Immunocompromised Host*
  • Immunohistochemistry
  • Methylprednisolone / therapeutic use
  • Middle Aged
  • Mycophenolic Acid / analogs & derivatives
  • Pemphigus / diagnosis
  • Pemphigus / drug therapy
  • Pemphigus / immunology*
  • Risk Assessment
  • Severity of Illness Index
  • Skin Diseases, Vascular / drug therapy
  • Skin Diseases, Vascular / immunology
  • Skin Diseases, Vascular / pathology*
  • Treatment Outcome

Substances

  • Mycophenolic Acid
  • Methylprednisolone