Early treatment suppresses the development of spike-wave epilepsy in a rat model

Epilepsia. 2008 Mar;49(3):400-9. doi: 10.1111/j.1528-1167.2007.01458.x. Epub 2007 Dec 6.

Abstract

Purpose: Current treatments for epilepsy may control seizures, but have no known effects on the underlying disease. We sought to determine whether early treatment in a model of genetic epilepsy would reduce the severity of the epilepsy phenotype in adulthood.

Methods: We used Wistar albino Glaxo rats of Rijswijk (WAG/Rij) rats, an established model of human absence epilepsy. Oral ethosuximide was given from age p21 to 5 months, covering the usual period in which seizures develop in this model (age approximately 3 months). Two experiments were performed: (1) cortical expression of ion channels Nav1.1, Nav1.6, and HCN1 (previously shown to be dysregulated in WAG/Rij) measured by immunocytochemistry in adult treated rats; and (2) electroencephalogram (EEG) recordings to measure seizure severity at serial time points after stopping the treatment.

Results: Early treatment with ethosuximide blocked changes in the expression of ion channels Nav1.1, Nav1.6, and HCN1 normally associated with epilepsy in this model. In addition, the treatment led to a persistent suppression of seizures, even after therapy was discontinued. Thus, animals treated with ethosuximide from age p21 to 5 months still had a marked suppression of seizures at age 8 months.

Discussion: These findings suggest that early treatment during development may provide a new strategy for preventing epilepsy in susceptible individuals. If confirmed with other drugs and epilepsy paradigms, the availability of a model in which epileptogenesis can be controlled has important implications both for future basic studies, and human therapeutic trials.

Publication types

  • Comparative Study
  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Animals, Newborn / growth & development
  • Anticonvulsants / pharmacology*
  • Anticonvulsants / therapeutic use
  • Cerebral Cortex / drug effects
  • Cerebral Cortex / physiology
  • Cerebral Cortex / physiopathology
  • Cyclic Nucleotide-Gated Cation Channels / drug effects
  • Cyclic Nucleotide-Gated Cation Channels / genetics
  • Disease Models, Animal
  • Electroencephalography / drug effects*
  • Electroencephalography / statistics & numerical data
  • Epilepsy, Absence / genetics*
  • Epilepsy, Absence / physiopathology
  • Epilepsy, Absence / prevention & control*
  • Ethosuximide / pharmacology*
  • Ethosuximide / therapeutic use
  • Female
  • Humans
  • Hyperpolarization-Activated Cyclic Nucleotide-Gated Channels
  • Ion Channels / drug effects
  • Ion Channels / genetics
  • NAV1.1 Voltage-Gated Sodium Channel
  • NAV1.6 Voltage-Gated Sodium Channel
  • Nerve Tissue Proteins / drug effects
  • Nerve Tissue Proteins / genetics
  • Phenotype
  • Potassium Channels / drug effects
  • Potassium Channels / genetics
  • Rats
  • Rats, Wistar
  • Severity of Illness Index
  • Sodium Channels / drug effects
  • Sodium Channels / genetics

Substances

  • Anticonvulsants
  • Cyclic Nucleotide-Gated Cation Channels
  • HCN1 protein, human
  • Hcn1 protein, rat
  • Hyperpolarization-Activated Cyclic Nucleotide-Gated Channels
  • Ion Channels
  • NAV1.1 Voltage-Gated Sodium Channel
  • NAV1.6 Voltage-Gated Sodium Channel
  • Nerve Tissue Proteins
  • Potassium Channels
  • SCN1A protein, human
  • Scn1a protein, rat
  • Scn8a protein, rat
  • Sodium Channels
  • Ethosuximide