Successful treatment with plasma exchange in adult-onset Still's disease with hyper-IL-18-naemia and hyperallergic state

Mod Rheumatol. 2008;18(4):407-10. doi: 10.1007/s10165-008-0065-9. Epub 2008 Apr 29.

Abstract

Adult-onset Still's disease (AOSD) is a rheumatoid disorder characterized by high fever, polyarthritis, leukocytosis, hyperferritinaemia, and mild liver involvement. We describe the case of a patient with AOSD with severe liver dysfunction. His serum levels of interleukin-10 and 18 showed a similar trend to his disease activity. Drug lymphocyte stimulation tests were positive for three drugs in the patient. Hypercytokinaemia was controlled by plasma exchange therapy.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Drug Hypersensitivity / complications
  • Drug Hypersensitivity / therapy*
  • Humans
  • Interferon-gamma / blood
  • Interleukin-18 / blood*
  • Interleukin-6 / blood
  • Male
  • Plasma Exchange
  • Still's Disease, Adult-Onset / complications
  • Still's Disease, Adult-Onset / therapy*

Substances

  • IL6 protein, human
  • Interleukin-18
  • Interleukin-6
  • Interferon-gamma