[Primary bilateral adrenal T-cell lymphoma. A case report rarer than B-cell lymphoma]

Ann Endocrinol (Paris). 2008 Jun;69(3):249-53. doi: 10.1016/j.ando.2007.12.002. Epub 2008 May 1.
[Article in French]

Abstract

Primary adrenal lymphoma is a rare condition. Only 70 cases were described in the literature. Adrenal lymphoma is often bilateral and in most of the cases of B-cell type. T-cell lymphoma is exceptional. The prognosis is bad and patient can die early because of acute adrenal insufficiency. We report a case of a 70-year-old man who was admitted for acute adrenal insufficiency due to primary bilateral adrenal T-cell lymphoma. He had corticotherapy and surgical exploration for intra-abdominal sepsis. He died because of multivisceral deficiency. Clinical features and imaging are not specific. (18)F-FDG PET Scan is an excellent mean to detect malignant tumor of adrenal gland. Percutaneous needle biopsy is useful to determine histology. The standard treatment is chemotherapy.

Publication types

  • Case Reports

MeSH terms

  • Adrenal Gland Neoplasms / diagnostic imaging*
  • Adrenal Gland Neoplasms / pathology
  • Aged
  • Fatal Outcome
  • Fluorodeoxyglucose F18
  • Humans
  • Immunohistochemistry
  • Incidence
  • Lymphoma, B-Cell / epidemiology
  • Lymphoma, T-Cell / diagnostic imaging*
  • Lymphoma, T-Cell / epidemiology
  • Lymphoma, T-Cell / pathology
  • Male
  • Multiple Organ Failure
  • Positron-Emission Tomography
  • Radiopharmaceuticals

Substances

  • Radiopharmaceuticals
  • Fluorodeoxyglucose F18