CD8+ epidermotropic cytotoxic T-cell lymphoma with peripheral blood and central nervous system involvement

Arch Dermatol. 2008 Aug;144(8):1027-9. doi: 10.1001/archderm.144.8.1027.

Abstract

Background: Most cutaneous T-cell lymphomas demonstrate a malignant population with a CD4(+) phenotype. In rare cases, CD8(+) phenotypes have been described based on immunostaining of skin specimens. Although some CD8(+) lymphomas have an indolent course, others, such as CD8(+) epidermotropic cytotoxic T-cell lymphomas, are typically more aggressive. To our knowledge, involvement of peripheral blood or cerebrospinal fluid with a malignant population of CD8(+) cells demonstrated by flow cytometry and T-cell receptor gene rearrangement has not been previously described.

Observations: We describe a patient with a CD8(+) cutaneous T-cell lymphoma with an initially indolent course and early stage diagnosed on the basis of a skin biopsy specimen. However, when flow cytometry was performed looking specifically at CD8(+)/CD4(-) cells in the peripheral blood and cerebrospinal fluid, a malignant population of CD8(+)/CD4(-)/CD26(-)/CD7(-) cells was discovered.

Conclusions: It is important for prognosis and treatment to be able to identify CD8(+) epidermotropic cytotoxic T-cell lymphoma and separate it from other relatively indolent CD8(+) lymphomas. Furthermore, detection of an abnormal CD8(+)/CD26(-)/CD7(-) T-cell population within the peripheral blood has important prognostic and therapeutic implications. The use of flow cytometry looking for abnormal CD8(+) populations in the peripheral blood or cerebrospinal fluid can assist with this critical information.

Publication types

  • Case Reports

MeSH terms

  • Aged
  • Antigens, CD / metabolism
  • Central Nervous System Neoplasms / immunology
  • Cerebrospinal Fluid / immunology
  • Female
  • Flow Cytometry
  • Gene Rearrangement, T-Lymphocyte
  • Humans
  • Immunophenotyping
  • Leukemia / immunology
  • Lymphoma, T-Cell, Cutaneous / diagnosis
  • Lymphoma, T-Cell, Cutaneous / immunology*
  • Prognosis
  • Skin / pathology
  • Skin Neoplasms / diagnosis
  • Skin Neoplasms / immunology*
  • T-Lymphocytes, Cytotoxic* / metabolism

Substances

  • Antigens, CD