Serial diffusion imaging in a case of mitochondrial encephalomyopathy, lactic acidosis, and stroke-like episodes

Stroke. 2009 Feb;40(2):e15-7. doi: 10.1161/STROKEAHA.108.523118. Epub 2008 Dec 18.

Abstract

Background and purpose: Most diffusion MRI studies of mitochondrial encephalomyopathy, lactic acidosis, and stroke-like episode stroke-like lesions report high- or normal-apparent diffusion coefficient, and this has been used to differentiate stroke-like lesion from ischemic stroke. There are, however, 3 recent reports of restricted diffusion in the acute phase of the stroke-like lesions. The purpose of our study was to investigate this apparent paradox.

Methods: We performed 9 serial MRI covering 2 stroke-like episodes in a 36-year-old man with mitochondrial encephalomyopathy, lactic acidosis, and stroke-like episode caused by the common mitochondrial DNA mutation 3243A>G.

Results: We found clear evidence of initial restricted diffusion in the stroke-like lesions, which gradually evolved to high-apparent diffusion coefficient as lesions aged. Evolution was, however, asynchronous with both high- and low-apparent diffusion coefficients temporally coexisting.

Conclusions: Our findings suggest that cytotoxic edema does occur early in the course of a stroke-like lesions and that its presence or, conversely, the absence of vasogenic edema, should not weaken the possibility of mitochondrial encephalomyopathy, lactic acidosis, and stroke-like episode in favor of ischemic stroke.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Brain / pathology
  • Brain Edema / pathology
  • DNA / genetics
  • Diffusion Magnetic Resonance Imaging / methods*
  • Disease Progression
  • Humans
  • Image Processing, Computer-Assisted
  • MELAS Syndrome / complications
  • MELAS Syndrome / genetics
  • MELAS Syndrome / pathology*
  • Male
  • Mutation

Substances

  • DNA