In vivo imaging of the mouse model of X-linked juvenile retinoschisis with fourier domain optical coherence tomography

Invest Ophthalmol Vis Sci. 2009 Jun;50(6):2989-93. doi: 10.1167/iovs.08-2542. Epub 2009 Jan 31.

Abstract

Purpose: The purpose of this study was to investigate Fourier domain optical coherence tomography (FD OCT) as a noninvasive tool for retinal imaging in the Rs1h-knockout mouse (model for X-linked juvenile retinoschisis).

Methods: A prototype spectrometer-based FD OCT system was used in combination with a custom optical beam-scanning platform. Images of the retinas from wild-type and Rs1h-knockout mice were acquired noninvasively with FD OCT with the specimen anesthetized. At the completion of the noninvasive FD OCT imaging, invasive retinal cross-sectional images (histology) were acquired from a nearby region for comparison to the FD OCT images.

Results: The retinal layers were identifiable in the FD OCT images, permitting delineation and thickness measurement of the outer nuclear layer (ONL). During FD OCT in vivo imaging of the Rs1h-knockout mouse, holes were observed in the inner nuclear layer (INL), and retinal cell disorganization was observed as a change in the backscattering intensity profile. Comparison of the ONL measurements acquired noninvasively with FD OCT to measurements taken using histology at nearby locations showed a degeneration of roughly 30% of the ONL by the age of 2 months in Rs1h-knockout mice relative to wild-type.

Conclusions: FD OCT was demonstrated to be effective for noninvasive imaging of retinal degeneration and observation of retinal holes in Rs1h-knockout mice.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Body Weights and Measures
  • Cell Adhesion Molecules / genetics
  • Diagnostic Techniques, Ophthalmological*
  • Disease Models, Animal*
  • Eye Proteins / genetics
  • Fourier Analysis*
  • Mice
  • Mice, Knockout
  • Microscopy, Fluorescence
  • Retinal Neurons / pathology
  • Retinoschisis / genetics
  • Retinoschisis / pathology*
  • Tomography, Optical Coherence*

Substances

  • Cell Adhesion Molecules
  • Eye Proteins
  • RS1 protein, mouse