Double-orifice mitral valve associated with bicuspid aortic valve: a rare case of incomplete form of Shone's complex

Eur J Echocardiogr. 2009 Aug;10(6):801-3. doi: 10.1093/ejechocard/jep067. Epub 2009 Jun 6.

Abstract

Double-orifice mitral valve (DOMV) is a rare congenital malformation characterized by two separate valve orifices of varying sizes in association with the abnormalities of the subvalvular apparatus. It has been reported to be associated with a variety of other congenital malformations. We report a rare case of incomplete form of Shone's complex composed of a complete bridge-type DOMV and bicuspid aortic valve, well demonstrated by both transthoracic and transoesophageal echocardiography and cardiac magnetic resonance imaging.

Publication types

  • Case Reports

MeSH terms

  • Adult
  • Aortic Valve / abnormalities*
  • Aortic Valve / diagnostic imaging
  • Echocardiography
  • Echocardiography, Transesophageal
  • Heart Defects, Congenital / diagnostic imaging*
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Mitral Valve / abnormalities*
  • Mitral Valve / diagnostic imaging