Neuroblastoma originating from extra-abdominal sites: association with favorable clinical and biological features

J Korean Med Sci. 2009 Jun;24(3):461-7. doi: 10.3346/jkms.2009.24.3.461. Epub 2009 Jun 12.

Abstract

Neuroblastomas originating from different sites might have different clinical and biological characteristics. In the present study, the clinical (age, sex and stage) and biological (N-myc amplification, Shimada pathology and levels of lactate dehydrogenase, ferritin and neuron-specific enolase) characteristics of patients with newly diagnosed neuroblastoma were compared according to the site of tumor origin (extra-abdominal versus abdominal). The event-free survival rate (EFS) was also compared between the two groups. Among 143 neuroblastomas, 115 tumors originated from the abdomen, 26 from extra-abdominal sites and 2 from unknown primary sites. Frequencies of stage 4 tumor and N-myc amplified tumor were lower in the extra-abdominal group than in the abdominal group (34.6% vs. 60.0%, P=0.019 and 4.2% vs. 45.0%, P<0.001, respectively). Levels of lactate dehydrogenase, ferritin and neuron-specific enolase were significantly lower in the extra-abdominal group than in the abdominal group. The probability of 5-yr EFS (+/-95% confidence interval) was higher in the extra-abdominal group than in the abdominal group (94.4+/-10.6% vs. 69.4+/-9.4%, P=0.026). Taken together, neuroblastomas originating from extra-abdominal sites might be associated with more favorable clinical and biological characteristics and a better outcome than neuroblastomas originating from abdomen.

Keywords: Neuroblastoma; Prognosis; Thorax; Transplantation, Autologous.

MeSH terms

  • Disease-Free Survival
  • Female
  • Ferritins / blood
  • Humans
  • L-Lactate Dehydrogenase / blood
  • Male
  • Neuroblastoma / diagnosis*
  • Neuroblastoma / therapy
  • Phosphopyruvate Hydratase / blood
  • Prognosis
  • Treatment Outcome
  • Vanilmandelic Acid / urine

Substances

  • Vanilmandelic Acid
  • Ferritins
  • L-Lactate Dehydrogenase
  • Phosphopyruvate Hydratase