Detection of Hb Constant Spring by a capillary electrophoresis method

Hemoglobin. 2010 Jan;34(2):175-8. doi: 10.3109/03630261003680191.

Abstract

Hb Constant Spring [Hb CS; alpha142, Term-->Gln (TAA>CAA in alpha2)] is the most prevalent nondeletional alpha-thalassemia (alpha-thal) anomaly in southern China. In conjunction with alpha(0)-thal, it can cause severe Hb H (beta(4)) disease. The present study was done to evaluate the efficiency of two diagnostic methods in detecting Hb CS. Automated high performance liquid chromatography (HPLC) and Sebia Capillarys 2, a capillary electrophoresis method, were applied to blood samples from 21 individuals with Hb CS trait. Of the 21 cases, all (100%) were detected by capillary electrophoresis, whereas only 16 (76.2%) were detected by HPLC. We concluded that the Sebia Capillarys 2 is the preferred method for Hb CS screening.

Publication types

  • Comparative Study
  • Evaluation Study

MeSH terms

  • Adult
  • Blood Protein Electrophoresis / methods*
  • Child
  • Chromatography, High Pressure Liquid / methods*
  • Electrophoresis, Capillary / methods*
  • Female
  • Hemoglobins, Abnormal / analysis*
  • Humans
  • Male
  • Mass Screening / methods
  • alpha-Thalassemia / blood*
  • alpha-Thalassemia / diagnosis

Substances

  • Hemoglobins, Abnormal
  • Hemoglobin Constant Spring