The architecture of respiratory complex I

Nature. 2010 May 27;465(7297):441-5. doi: 10.1038/nature09066.

Abstract

Complex I is the first enzyme of the respiratory chain and has a central role in cellular energy production, coupling electron transfer between NADH and quinone to proton translocation by an unknown mechanism. Dysfunction of complex I has been implicated in many human neurodegenerative diseases. We have determined the structure of its hydrophilic domain previously. Here, we report the alpha-helical structure of the membrane domain of complex I from Escherichia coli at 3.9 A resolution. The antiporter-like subunits NuoL/M/N each contain 14 conserved transmembrane (TM) helices. Two of them are discontinuous, as in some transporters. Unexpectedly, subunit NuoL also contains a 110-A long amphipathic alpha-helix, spanning almost the entire length of the domain. Furthermore, we have determined the structure of the entire complex I from Thermus thermophilus at 4.5 A resolution. The L-shaped assembly consists of the alpha-helical model for the membrane domain, with 63 TM helices, and the known structure of the hydrophilic domain. The architecture of the complex provides strong clues about the coupling mechanism: the conformational changes at the interface of the two main domains may drive the long amphipathic alpha-helix of NuoL in a piston-like motion, tilting nearby discontinuous TM helices, resulting in proton translocation.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Benzoquinones / metabolism
  • Binding Sites
  • Cell Membrane / metabolism
  • Crystallography, X-Ray
  • Electron Transport Complex I / chemistry*
  • Electron Transport Complex I / metabolism*
  • Escherichia coli / enzymology*
  • Models, Molecular
  • Protein Structure, Secondary
  • Protein Structure, Tertiary
  • Protein Subunits / chemistry*
  • Protein Subunits / metabolism*
  • Structure-Activity Relationship
  • Thermus thermophilus / enzymology*

Substances

  • Benzoquinones
  • Protein Subunits
  • quinone
  • Electron Transport Complex I

Associated data

  • PDB/3M9C
  • PDB/3M9S