Expansion of myelin autoreactive CD8+ T lymphocytes in patients with neuropsychiatric systemic lupus erythematosus

Ann Rheum Dis. 2011 May;70(5):868-71. doi: 10.1136/ard.2010.140012. Epub 2010 Dec 27.

Abstract

Objectives: Delineation of mechanisms underlying neuropsychiatric systemic lupus erythematosus (NPSLE) and determination of biological markers could guide treatment choice. A study was undertaken to analyse the potential role of activated CD8+ T cells in NPSLE as previously reported in SLE nephritis.

Methods: Flow cytometric immunophenotyping of blood lymphocytes was performed in 30 patients with NPSLE and 36 healthy individuals. The antigenic specificity of CD8+ T cells was studied using HLA-A0201 tetramers loaded with several myelin-derived peptides. The intracellular level of interferon γ (IFNγ) produced by activated CD8+ T cells was determined by flow cytometry.

Results: A large increase in circulating activated CD8+ T lymphocytes expressing surface HLA-DR was found in patients with NPSLE without antiphospholipid syndrome (APS) (n=18) compared with patients with APS (n=12) or healthy controls (n=36). IFNγ-secreting myelin-specific CD8+ T cells were detected exclusively in the blood of patients with NPSLE without APS but with white matter lesions.

Conclusions: These data strongly support the existence of a new immune effector mechanism responsible for CNS involvement in patients with NPSLE and suggest that analysing HLA-DR expression combined with myelin-specific tetramer staining on CD8+ T lymphocytes may be a valuable additional tool for the monitoring of these patients.

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • CD8-Positive T-Lymphocytes / immunology*
  • Case-Control Studies
  • Female
  • HLA-DR Antigens / blood
  • Humans
  • Immunophenotyping
  • Interferon-gamma / biosynthesis
  • Lupus Vasculitis, Central Nervous System / immunology*
  • Lymphocyte Activation / immunology
  • Male
  • Middle Aged
  • Myelin Sheath / immunology*
  • Young Adult

Substances

  • HLA-DR Antigens
  • Interferon-gamma