Genome-wide functions of PML-RARα in acute promyelocytic leukaemia

Br J Cancer. 2011 Feb 15;104(4):554-8. doi: 10.1038/sj.bjc.6606095. Epub 2011 Jan 18.

Abstract

PML-RAR (retinoic acid receptor)α is the hallmark protein of acute promyelocytic leukaemia, a highly malignant subtype of acute myeloid leukaemia that accounts for approximately 10% of all AML cases. Recently, several studies have been set out to obtain a comprehensive genome-wide view of the molecular actions of this chimeric protein. In this review, we highlight the new insights that arose from these studies, in particular focussing on newly identified PML-RARα target genes, its interplay with RXR and deregulation of epigenetic modifications.

Publication types

  • Research Support, Non-U.S. Gov't
  • Review

MeSH terms

  • Animals
  • Epigenesis, Genetic / physiology
  • Genome, Human*
  • Humans
  • Leukemia, Promyelocytic, Acute / genetics*
  • Models, Biological
  • Oncogene Proteins, Fusion / genetics
  • Oncogene Proteins, Fusion / physiology*
  • Signal Transduction / genetics
  • Signal Transduction / physiology

Substances

  • Oncogene Proteins, Fusion
  • promyelocytic leukemia-retinoic acid receptor alpha fusion oncoprotein